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Inherited Metabolic Disorders and a Low Protein Diet

A number of inherited metabolic disorders are treated with a low protein diet. These include phenylketonuria (PKU), branched chain ketoaciduria or Maple Syrup Urine disease (MSUD), tyrosinemia, methylmalonic acidemia (MMA), propionicacidemia (PPA), homocystinuria, and urea cycle disorders, among others. These metabolic disorders require low protein diets to prevent a variety of symptoms, including mental retardation and neurological problems. For some, the low protein diet is life-saving.

Everyone with one of these inherited metabolic disorders must have a specific diet, planned in accordance their metabolic tolerance. The diet must be supervised by a qualified nutritionist or physician knowledgeable about the condition, and must be monitored regularly through blood tests.

Apples to Zucchini: A Collection of Favorite Low Protein Recipes is the perfect resource to help you manage a low protein diet and discover the vast array of wonderful tasting and healthy foods that are naturally low in protein. The book will show you just how varied and interesting a low protein diet can be, using a wide variety of fruits and vegetables and only a limited number of commercially made low protein products.